https://www.ijmhr.org/ijpr.html editor_physiotherapy@hotmail.com
ISSN:       2321-1822 (E) 2321-8975 (P)

IJPR.2017.267

DOWNLOAD PDF
Table of Contents

Type of Article:  Case Report

Volume 6; Issue 1 (February 2018)

Page No.: 2623-2626

DOI: https://dx.doi.org/10.16965/ijpr.2017.267

SPINAL ARTERIOVENOUS METAMERIC SYNDROME: ROLE OF PHYSIOTHERAPY: A CASE REPORT

Binita Lama *1, Pallavi Wajapey 2, Ishwor Pyatha 3.

1 Student, RV College of Physiotherapy, Bangalore, Karnataka, India.

2 Assistant Professor, RV College of Physiotherapy, Bangalore, Karnataka, India.

3 Student,  RV College of Physiotherapy, Bangalore, Karnataka, India.

Address for Correspondence:  Binita Lama, RV College of Physiotherapy, Bangalore, Karnataka, India. E-Mail: bntaso7@gmail.com

ABSTRACT

Background: Spinal arteriovenous metameric syndrome (SAMS), also known as Cobb syndrome is a rare metameric developmental disorder presenting as an extradural-intradural vascular malformation that involves bone, muscle, skin, spinal cord, and nerve roots.

Case Report: An 11-year-old girl presented with history of progressive paraparesis, lower extremity sensory loss, along with bowel and bladder incontinence who was diagnosed with Cobb syndrome. She underwent endovascular embolization of one arterial feeder and two metameric components. Post embolization patient experienced further decline in muscle strength. Physiotherapy regimen was implemented for 4-5 days per week for period of two months. The patient was discharged with a home exercise programme.

Result: At the time of discharge, muscle power was improved. Patient was able to walk with the help of walker.

Conclusion: Spinal metameric arteriovenous syndrome is a complex nonhereditary genetic vascular disorder associated with variety of neurologic deficits. Physiotherapy management will play a major role in minimizing disability hence improve clinical outcome.

KEY WORDS: Spinal Arteriovenous Metameric Syndrome, Progressive Paraparesis, Embolization, Physiotherapy.

REFERENCES

  1. Komiyama M, Ishiguro T, Terada A, Watanabe Y et al. Spinal arteriovenous metameric syndrome in a neonate presenting with congestive heart failure: case report. Childs Nerv Syst. 31 May 2017;30(9):1607-1611.
  2. Maramattom BV, Cohen-Gadol AA, Wijdicks EF, et al. Segmental cutaneous hemangioma and spinal arteriovenous malformation (Cobb syndrome). Case report and historical perspective. J Neurosurg Spine. 2005; 3: 249–52.
  3. Miyatake S, Kikuchi H, Koide T, et al. Cobb’s syndrome and its treatment with embolization. J Neurosurg. 1990; 72: 497–9.
  4. PalP, Ray S, Chakraborty S, Dey S, Talukdar A. Cobb syndrome: A rare cause of paraplegia. Annals of Neurosciences. 2015;22(3).
  5. MatsumaruY, PongpechS, LaothamasJ, etal. Multifocal and metameric spinal cord arteriovenous malformations: review of 19 cases. Interv Neuroradiol. 1999;5:27–34.
  6. Niimi, N. Uchiyama, L. Elijovich and A. Berenstein Spinal Arteriovenous Metameric Syndrome: Clinical Manifestations and Endovascular Management American Journal of Neuroradiology February 2013; 34(2):457-463. DOI: https://doi.org/10.3174/ajnr.A3212
  7. Clark MT, Brooks EL, Chong W, Pappas C, Fahey M: Cobb syndrome: a case report and systematic review of the literature. Pediatr Neurol. 2008;39:423–425.
  8. Dilmé-Carreras E, Iglesias-Sancho M, Márquez-Balbás G, Sola-Ortigosa J, Umbert-Millet P: Cobb syndrome: case report and review of the literature. Dermatology. 2010;221:110–112.
  9. Jessen RT, Thompson S, Smith EB: Cobb syndrome. Arch Dermatol. 1997;113:1587–1590.

Cite this article: Binita Lama, Pallavi Wajapey, Ishwor Pyatha. SPINAL ARTERIOVENOUS METAMERIC SYNDROME: ROLE OF PHYSIOTHERAPY: A CASE REPORT. Int J Physiother Res 2018;6(1):2623-2626. DOI: 10.16965/ijpr.2017.267
Post Views: 0