Type of Article:  Case Report

Volume 6; Issue 1 (February 2018)

Page No.: 2623-2626

DOI: https://dx.doi.org/10.16965/ijpr.2017.267


Binita Lama *1, Pallavi Wajapey 2, Ishwor Pyatha 3.

1 Student, RV College of Physiotherapy, Bangalore, Karnataka, India.

2 Assistant Professor, RV College of Physiotherapy, Bangalore, Karnataka, India.

3 Student,  RV College of Physiotherapy, Bangalore, Karnataka, India.

Address for Correspondence:  Binita Lama, RV College of Physiotherapy, Bangalore, Karnataka, India. E-Mail: bntaso7@gmail.com


Background: Spinal arteriovenous metameric syndrome (SAMS), also known as Cobb syndrome is a rare metameric developmental disorder presenting as an extradural-intradural vascular malformation that involves bone, muscle, skin, spinal cord, and nerve roots.

Case Report: An 11-year-old girl presented with history of progressive paraparesis, lower extremity sensory loss, along with bowel and bladder incontinence who was diagnosed with Cobb syndrome. She underwent endovascular embolization of one arterial feeder and two metameric components. Post embolization patient experienced further decline in muscle strength. Physiotherapy regimen was implemented for 4-5 days per week for period of two months. The patient was discharged with a home exercise programme.

Result: At the time of discharge, muscle power was improved. Patient was able to walk with the help of walker.

Conclusion: Spinal metameric arteriovenous syndrome is a complex nonhereditary genetic vascular disorder associated with variety of neurologic deficits. Physiotherapy management will play a major role in minimizing disability hence improve clinical outcome.

KEY WORDS: Spinal Arteriovenous Metameric Syndrome, Progressive Paraparesis, Embolization, Physiotherapy.


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Cite this article: Binita Lama, Pallavi Wajapey, Ishwor Pyatha. SPINAL ARTERIOVENOUS METAMERIC SYNDROME: ROLE OF PHYSIOTHERAPY: A CASE REPORT. Int J Physiother Res 2018;6(1):2623-2626. DOI: 10.16965/ijpr.2017.267