POTTER’S SYNDROME: A CASE REPORT A.K.Manicka Vasuki * 1 , M.Nirmaladevi 2 , Deborah Joy Hebzibah 3 , M.Jamuna 4 , K.Radhika 5 ,  K.Kalyana Sundaram 6 . *1 Assistant Professor, Department of Anatomy, PSG Institute Of Medical Sciences And Research, Coimbatore, Tamil Nadu, India. 2  Associate Professor, Department of Anatomy, PSG Institute Of Medical Sciences And Research,  Coimbatore, Tamil Nadu, India. 3  Assistant Professor, Department of Anatomy, PSG Institute Of Medical Sciences And Research, Coimbatore, Tamil Nadu, India. 4  Professor and HOD, Department of Anatomy, PSG Institute Of Medical Sciences And Research, Coimbatore, Tamil Nadu, India. 5  Assistant Professor, Department of Anatomy, PSG Institute Of Medical Sciences And Research, Coimbatore, Tamil Nadu, India. 6  Associate Professor, Department of Anaesthesiology, Coimbatore Medical College, Coimbatore, Tamil Nadu, India. Address   for   correspondence:    Dr.A.K.Manicka   Vasuki,   Assistant   Professor,   Anatomy   Department,   PSG   Institute   Of   Medical   Sciences   and   Research, Coimbatore, Tamil Nadu, India. E-Mail:  vasukikalyan01@gmail.com ABSTRACT: Renal   agenesis   occurs   as   a   result   from   a   lack   of   induction   of   metanephric   blastema   by   the   ureteral   bud.   This   may   be   secondary   to   defect   in   the   formation   of mesonephric   duct   or   ureteral   bud   maldevelopment.   Postnatal   involution   of   multicystic   kidneys   may   also   result   in   solitary   kidney.   This   may   be   associated with   VACTERL   SYNDROME   or   may   be   associated   with   ipsilateral   urogenital   anomalies.   During   dissection   of   19   weeks   old   male   fetus   in   the   department   of Anatomy,   We   found   bilateral   renal   agenesis   with   Pulmonary   hypoplasia.   Prenatal   ultrasound   showed   Oligohydramnios   with   bilateral   renal   agenesis. Bilateral   renal   agenesis   may   also   be   associated   with   pulmonary   hypoplasia.   The   newborn   would   die   shortly   after   birth,   due   to   severe   pulmonary   hypoplasia. Hence   we   have   to   look   for   other   anomalies   in   renal   agenesis.   The   risk   of   other   anomalies   in   the   subsequent   pregnancy   is   also   increased   because   the condition may be an autosomal dominant or recessive disorder. KEY WORDS: Agenesis of kidney, fetus, pulmonary hypoplasia, oligohydramnios References 1 . Hetel   Parikh,   Sameer   Raniga   et   al,   Antenatal   diagnosis   of   Bilateral   renal   agenesis   with   Potter’s   sequence:   A   rare   case,   I.J.Clinical   Practice,Mar 2012;22(10):526-28. 2 . A.Mishra, Renal agenesis : report of an interesting case, BJR, Aug 2007;80(956):167-69. 3 . Prashin C.Unadkat, Radha verma et al, Right undescended testis with ipsilateral renal agenesis, I.J.Sci.Study, Oct 2014;2(7):240-41. 4 . Maki   Kashiwagi,   Rabih   Chaoni   et   al,   Fetal   bilateral   renal   agenesis,   Phocomelia   and   single   umbilical   artery   associated   with   cocaine   abuse   in   early pregnancy, Birth defects Research (Part A),2003;67:951-52. 5 . Abdelmageed Abdelrahman, A case of Uterus didelphys and unilateral renal agenesis, Sudan Med.J, Apr 2013;49(1):41-43. 6 . Doron   Kabiri,   Yaara   Arzy   etal,   Herlyn   –   Werner   –   Wuderlich   syndrome:   uterus   didelphys   and   obstructive   hemivagina   with   unilateral   renal   agenesis, IMAJ,Jan2013;15:66. 7 . A.Nickavar, M.Razzaghy – Azar et al, Pheochromocytoma and renal agenesis, Acta Medica Iranica,2008;46(1):81-83. 8 . Shreeprasad.P.Patankar, Vijay Kalrao,et al. Mayer – Rokitansky syndrome with Anorectal malformation, I.J.Pediatrics, Dec 2013;71(12):1133-35. 9 . Anas M.Ajazami, Ranad Shaheen et al, Am.J.um.Genet.,Sep.2011;85(3):414-18.